Cardiac effects of OPA1 protein promotion in a transgenic animal model

PLoS One. 2024 Nov 21;19(11):e0310394. doi: 10.1371/journal.pone.0310394. eCollection 2024.

Abstract

Mitochondria form a dynamic network in cells, regulated by the balance between mitochondrial fusion and fission. The inhibition of mitochondrial fission can have positive effects in acute ischemic/reperfusion injury models by preventing the fall in mitochondrial membrane potential associated with fission processes. However, inhibition of fission in chronic models is disadvantageous because it obstructs the elimination of damaged mitochondrial fragments. OPA1, in view of previous results, is a possible therapeutic target as a fusion promoter and structure stabilizer protein. We used transgenic mice in which the OMA1 cleavage sites of OPA1 were deleted. This resulted in a higher representation of L-OPA1 compared to S-OPA1. After genotyping and model validation, all animals were examined by echocardiograph on two occasions, at weeks 11 and 36. Histological samples were taken from hearts to examine mitochondrial morphology and structure remodeling. The signaling pathways related to mitochondrial dynamic processes were evaluated. Cardiomyocytes were isolated from neonatal mice to determine the efficiency of mitochondrial respiration using the SeaHorse assay method. OPA1 protein promotion has a negative effect on systolic function during aging. We confirmed that volume overload and ventricular remodeling did not manifest. The reason behind the loss of pump function might be, at least partly, due to the energy deficit caused by mitochondrial respiratory failure and damage in mitochondrial quality control pathways.

MeSH terms

  • Animals
  • GTP Phosphohydrolases* / genetics
  • GTP Phosphohydrolases* / metabolism
  • Mice
  • Mice, Transgenic*
  • Mitochondria, Heart / metabolism
  • Mitochondrial Dynamics
  • Myocytes, Cardiac* / metabolism
  • Ventricular Remodeling

Substances

  • Opa1 protein, mouse
  • GTP Phosphohydrolases

Grants and funding

The research in Hungary was funded by NKFIH within the framework of the University of Pécs' project TKP2021-EGA-17.