α-Synuclein seeding amplification assays for diagnosing synucleinopathies: an innovative tool in clinical implementation

Transl Neurodegener. 2024 Nov 21;13(1):56. doi: 10.1186/s40035-024-00449-2.

Abstract

The spectrum of synucleinopathies, including Parkinson's disease (PD), multiple system atrophy (MSA), and dementia with Lewy bodies (DLB), is characterized by α-synuclein (αSyn) pathology, which serves as the definitive diagnostic marker. However, current diagnostic methods primarily rely on motor symptoms that manifest years after the initial neuropathological changes, thereby delaying potential treatment. The symptomatic overlap between PD and MSA further complicates the diagnosis, highlighting the need for precise and differential diagnostic methods for these overlapping neurodegenerative diseases. αSyn misfolding and aggregation occur before clinical symptoms appear, suggesting that detection of pathological αSyn could enable early molecular diagnosis of synucleinopathies. Recent advances in seed amplification assay (SAA) offer a tool for detecting neurodegenerative diseases by identifying αSyn misfolding in fluid and tissue samples, even at preclinical stages. Extensive research has validated the effectiveness and reproducibility of SAAs for diagnosing synucleinopathies, with ongoing efforts focusing on optimizing conditions for detecting pathological αSyn in more accessible samples and identifying specific αSyn species to differentiate between various synucleinopathies. This review offers a thorough overview of SAA technology, exploring its applications for diagnosing synucleinopathies, addressing the current challenges, and outlining future directions for its clinical use.

Keywords: Diagnosis; Movement disorders; Quiescent seed amplification assay; Seed amplification assay; α-Synuclein.

Publication types

  • Review

MeSH terms

  • Humans
  • Lewy Body Disease / diagnosis
  • Lewy Body Disease / genetics
  • Lewy Body Disease / metabolism
  • Multiple System Atrophy / diagnosis
  • Multiple System Atrophy / genetics
  • Multiple System Atrophy / metabolism
  • Parkinson Disease / diagnosis
  • Parkinson Disease / genetics
  • Parkinson Disease / metabolism
  • Synucleinopathies* / diagnosis
  • Synucleinopathies* / genetics
  • Synucleinopathies* / metabolism
  • alpha-Synuclein* / analysis
  • alpha-Synuclein* / genetics
  • alpha-Synuclein* / metabolism

Substances

  • alpha-Synuclein