Single-Cell Transcriptomic Dataset of RPGR-associated Retinitis Pigmentosa Patient-Derived Retinal Organoids

Sci Data. 2024 Nov 26;11(1):1285. doi: 10.1038/s41597-024-04124-z.

Abstract

X-linked retinitis pigmentosa (XLRP) is a severe hereditary retinal disorder marked by progressive vision loss due to photoreceptor dysfunction. The retinitis pigmentosa GTPase regulator (RPGR) gene, responsible for most XLRP cases, encodes a protein crucial for the transport of visual signal proteins between the photoreceptor inner and outer segments. However, the mechanism of RPGR mutation causing photoreceptor disorder is not clear and effective treatments remain elusive. This study utilized retinal organoids (ROs) derived from normal and RPGR-mutant human induced pluripotent stem cells (hiPSC) at four developmental stages (40, 90, 150, and 200 days). Single-cell RNA sequencing (scRNA-seq) was conducted on 71,096 cells, including 33,839 cells from the control group and 37,257 cells from the RPGR group. Key retinal cell types were identified and the obtained scRNAseq dataset was validated reliable and high -quality. This study has provided data resources and references for exploring the mechanism of RPGR-related retinal degeneration and support the development of targeted therapies.

Publication types

  • Dataset

MeSH terms

  • Eye Proteins* / genetics
  • Humans
  • Induced Pluripotent Stem Cells* / metabolism
  • Mutation
  • Organoids*
  • Retina*
  • Retinitis Pigmentosa* / genetics
  • Single-Cell Analysis*
  • Transcriptome*

Substances

  • RPGR protein, human
  • Eye Proteins