A case of preaxial polydactyly and its surgical correction has been presented. The surgical management and postoperative complications were reviewed from the literature. The genetic basis for this type of polydactyly and its rate of occurrence were discussed. This patient's family exhibited an autosomal dominant gene with incomplete penetrance carried by the female members. The patient's family should be consulted regarding the possible genetic continuation of these anomalies in the female members of the family. The patient has had an unremarkable postoperative course with no reported adverse sequelae. The patient and surgeons were very satisfied with the final result. Figure 8 illustrates the surgical results 1 year postoperatively.