Effect of chloride ion on the oxygen affinity of hemoglobin York (alpha 2 beta 2(146)Pro) and S-York hybrid hemoglobin (alpha 2 beta S beta York). Role of the beta 82 lysyl and beta 146 histydyl residues in chloride binding to hemoglobin

J Biol Chem. 1983 Nov 25;258(22):13422-4.

Abstract

We estimated the relative role of various chloride binding sites in determining the oxygen affinity of hemoglobin using abnormal hemoglobins such as Hb York (Hb Y) (alpha 2 beta 2(146)Pro), Hb Malmö (Hb M) (alpha 2 beta 2(97)Gln), and Hb S and chemically modified hemoglobins such as cross-linked Hb S, Hb Y, and asymmetrical SY hemoglobin with bis(3,5-dibromosalicyl)fumarate. The chloride effect on the p50 values of Hb S and Hb M was identical to that of Hb A. In contrast, the effect of chloride on the p50 values of Hb Y was only 20% of that of Hb A. Cross-linking between the two beta 82 lysyl residues with fumarate decreased the chloride effect by 40%. The effect of chloride on cross-linked Hb Y, in which both beta 82 lysyl and beta 146 histidyl residues were modified, was unchanged from that on Hb Y (20% of Hb A). The effect of chloride on the p50 value of SY asymmetrical hybrid hemoglobin was 40% of that of Hb A or Hb S, which is midway between the values obtained for cross-linked Hb S and Hb Y. From these results, the contribution of beta 146 His and beta 82 Lys on oxygen affinity by binding of chloride was calculated to be 40% each; the remaining 20% chloride effect was attributed to alpha 1 Val.

Publication types

  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Chlorides / pharmacology*
  • Hemoglobin A / metabolism
  • Hemoglobin, Sickle / metabolism*
  • Hemoglobins, Abnormal / metabolism*
  • Histidine*
  • Humans
  • Kinetics
  • Lysine*
  • Macromolecular Substances
  • Oxygen / blood*
  • Proline*
  • Protein Binding

Substances

  • Chlorides
  • Hemoglobin, Sickle
  • Hemoglobins, Abnormal
  • Macromolecular Substances
  • Histidine
  • hemoglobin York
  • Hemoglobin A
  • Proline
  • Lysine
  • Oxygen