Polyclonal immunoglobulin secretion in patients with common variable immunodeficiency using monoclonal B cell differentiation factors

J Clin Invest. 1984 Dec;74(6):2115-20. doi: 10.1172/JCI111636.

Abstract

B cells from 25 patients with common variable immunodeficiency (CVI) were tested for their ability to differentiate under the influence of B cell differentiation factors (BCDF), derived from T cell hybridomas or T cell clones. 11 patients generated Ig plaque-forming cells in the range comparable to that of normal controls with supernatant from the T cell hybrid MOP 1L. With various hybrid or clone supernatants, differing response patterns emerged. Four patients who failed to respond to MOP 1L responded to T cell clone supernatant RAC. Another who failed to respond to both MOP 1L and RAC responded to T cell hybrid supernatant MTP 7. These results indicate that these supernatants contain different BCDFs and suggest heterogeneity in the differentiation states of B cells in CVI. In addition, three patients demonstrated exaggerated responses to BCDF, and evidence was obtained from B cells of these patients for increased BCDF receptor density. Thus, the accumulated evidence indicates that T cell defects may be a primary pathogenetic mechanism in common variable immunodeficiency, and purified BCDF may be of therapeutic value.

Publication types

  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Antigens, Differentiation, B-Lymphocyte
  • Antigens, Surface / immunology*
  • B-Lymphocytes / immunology*
  • Cell Differentiation
  • Humans
  • Immunologic Deficiency Syndromes / immunology*
  • Lymphocyte Activation
  • Pokeweed Mitogens / pharmacology
  • Time Factors

Substances

  • Antigens, Differentiation, B-Lymphocyte
  • Antigens, Surface
  • Pokeweed Mitogens