Freeze-fracture analysis of plasma membrane cholesterol in Duchenne muscle

Ann Neurol. 1983 May;13(5):532-5. doi: 10.1002/ana.410130510.

Abstract

We estimated cholesterol in Duchenne muscle plasma membrane using the sterol-specific ligand digitonin. In measuring the extent of digitonin-cholesterol complex formation with freeze-fracture electron microscopy, we found a significantly greater proportion of surface area taken up by complexes in Duchenne muscle (60% +/- 9%) than in controls (36% +/- 4%). This finding suggests that a population of Duchenne muscle fibers has a higher concentration of cholesterol in the plasma membrane. Membrane cholesterol is known to affect membrane deformability and the activity of membrane-bound enzymes and transport proteins; thus a difference in membrane cholesterol might account for structural and functional abnormalities in Duchenne plasma membrane.

Publication types

  • Research Support, Non-U.S. Gov't
  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Cell Membrane / metabolism
  • Cell Membrane / ultrastructure
  • Cholesterol / metabolism*
  • Digitonin / metabolism
  • Freeze Fracturing
  • Humans
  • Microscopy, Electron
  • Muscles / metabolism*
  • Muscles / ultrastructure
  • Muscular Dystrophies / metabolism*
  • Muscular Dystrophies / pathology

Substances

  • Cholesterol
  • Digitonin