Response to human acetylcholine receptor alpha 138-199: determinant spreading initiates autoimmunity to self-antigen in rabbits

Immunol Lett. 1994 Mar;39(3):269-75. doi: 10.1016/0165-2478(94)90168-6.

Abstract

NZW rabbits immunised with a mixture of synthetic peptides representing alpha 138-199 of the human acetylcholine receptor (AChR) alpha-subunit exhibited clinical, biochemical and electrophysiological signs of experimental autoimmune myasthenia gravis (EAMG), with raised levels of anti-rabbit AChR antibodies. Surprisingly, these were partly directed at the main immunogenic region (MIR, thought to be alpha 67-76) and alpha-Bungarotoxin binding sites on rabbit AChR, and reacted less well with human AChR. Moreover, they could be separated from the anti-peptide antibodies by fractionation on immobilised peptide. We conclude that immunisation with these peptides led, by 'determinant spreading', to a response directed at self-AChR. Similar phenomena may have been overlooked in previous studies of responses to synthetic or recombinant AChR sequences. These findings suggest that autoimmunity could be induced by low-affinity, cross-reacting epitopes even when the observed serum response is highly specific for the autoantigen.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Antibody Specificity / immunology
  • Autoimmunity / immunology*
  • Bungarotoxins / metabolism
  • Chromatography, Affinity
  • Epitopes / immunology*
  • Female
  • Humans
  • Myasthenia Gravis / immunology
  • Peptide Fragments / immunology
  • Precipitin Tests
  • Rabbits
  • Receptors, Cholinergic / immunology*
  • Receptors, Cholinergic / metabolism

Substances

  • Bungarotoxins
  • Epitopes
  • Peptide Fragments
  • Receptors, Cholinergic