The immunoglobulin VH gene, VH4-21, specifically encodes autoanti-red cell antibodies against the I or i antigens

Vox Sang. 1995;68(4):231-5. doi: 10.1111/j.1423-0410.1995.tb02578.x.

Abstract

Most autoanti-red cell antibodies found in patients with cold agglutinin disease are specific for the I or i carbohydrate antigenic determinants. However, antibodies specific for other antigens such as Pr or Sa can also be found, and these are identified by their pattern of reactivity with enzyme-treated red cells. Recently, it has been shown that the vast majority of anti-Ii antibodies react with a monoclonal anti-idiotypic antibody (9G4); this reactivity arises from restriction of the immunoglobulin heavy chains used to encode the antibodies to a single VH4-21 gene, VH4-21. The 9G4 antibody appears specific for this gene product, and we have used it to analyse VH4-21 gene involvement in encoding a spectrum of red cell antibodies of various specificities. The results support the strong association between usage of this gene and anti-Ii specificity and indicate that it is not generally used by other specificities. In particular, it is striking that the unsubstituted type 2 oligosaccharide antigens (I and i) induce a highly restricted autoantibody response very different from that induced by the sialylated type 2 antigens (Sia-b, -1 and 1b). The 9G4 antibody therefore provides a simple tool for discrimination between these autoanti-red cell antibodies, which should be of use in red cell serology.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adult
  • Agglutinins / immunology
  • Antibodies, Anti-Idiotypic / genetics
  • Antibodies, Anti-Idiotypic / immunology
  • Antibodies, Monoclonal / immunology
  • Antibody Specificity / genetics
  • Antibody Specificity / immunology
  • Autoantibodies / genetics*
  • Autoantibodies / immunology
  • Cryoglobulins
  • Enzyme-Linked Immunosorbent Assay / methods
  • Erythrocytes / immunology*
  • Genes, Immunoglobulin
  • Hemagglutination Inhibition Tests
  • Humans
  • I Blood-Group System / genetics*
  • I Blood-Group System / immunology
  • Immunoglobulin Heavy Chains / genetics*
  • Immunoglobulin Heavy Chains / immunology
  • Immunoglobulin Variable Region / genetics*
  • Immunoglobulin Variable Region / immunology

Substances

  • Agglutinins
  • Antibodies, Anti-Idiotypic
  • Antibodies, Monoclonal
  • Autoantibodies
  • Cryoglobulins
  • I Blood-Group System
  • Immunoglobulin Heavy Chains
  • Immunoglobulin Variable Region
  • cold agglutinins