Reduced IL-2 expression upon antigen stimulation is accompanied by deficient IL-9 gene expression in T cells of patients with CVID

Scand J Immunol. 1995 Mar;41(3):215-9. doi: 10.1111/j.1365-3083.1995.tb03556.x.

Abstract

Patients with common variable immunodeficiency (CVID) are heterogeneous in the clinical manifestation of the disease as well as in the underlying mechanisms leading to the immunodeficiency. In a previous study we identified a subgroup of patients with a primary immunodeficiency disease affecting IL-2 and IFN-gamma gene expression. The T cells of these patients revealed impaired proliferative response and reduced levels of IL-2 and IFN-gamma-specific mRNA after antigen stimulation in vitro, while cellular and molecular response to phorbol ester and the calcium ionophore ionomycin (PMA+IM) or anti-CD3 monoclonal antibodies (MoAbs) (OKT3) were comparable to those of healthy control individuals. Here we show that stimulation of these patients' T cells with tetanus toxoid (TT) resulted in dramatically reduced levels of IL-2, IL-9 and IFN-gamma mRNA, while IL-3 gene expression in three patients was comparable or even increased to the healthy controls. As expected, addition of exogenous IL-2 to tetanus toxoid pulsed cultures had virtually no effect on IL-2 transcription, but corrected the defect in IL-9 gene expression, while IFN-gamma mRNA levels were still reduced. In conclusion, these data suggest that recombinant IL-2 alone is not able to induce the IL-9 gene adequately in our patients, but clearly increases IL-9 mRNA levels in combination with tetanus toxoid.

MeSH terms

  • Antigens / immunology
  • Cells, Cultured
  • Common Variable Immunodeficiency / immunology*
  • Female
  • Gene Expression Regulation / immunology
  • Humans
  • Interferon-gamma / biosynthesis
  • Interleukin-2 / biosynthesis*
  • Interleukin-2 / pharmacology
  • Interleukin-3 / biosynthesis
  • Interleukin-9 / biosynthesis*
  • Lymphocyte Activation / immunology
  • Male
  • Receptors, Antigen, T-Cell / physiology
  • T-Lymphocytes / immunology*

Substances

  • Antigens
  • Interleukin-2
  • Interleukin-3
  • Interleukin-9
  • Receptors, Antigen, T-Cell
  • Interferon-gamma