The authors report on two cases of renal cell carcinoma in boys of 8 and 13 years of age revealed by gross hematuria. Following nephrectomy the evolution remains good after 8 and 17 years of follow-up. Despite the fact that renal cell carcinoma is rare in children, it must be evoked as a possible etiology in the presence of spontaneous and relapsing hematuria in a child older than 8 years of age. Early nephro-ureterectomy with regional lymph nodes resection is the only efficient treatment, chemotherapy and radiotherapy having not yet demonstrated their efficiency.