Heterogeneity of calcium channel autoantibodies detected using a small-cell lung cancer line derived from a Lambert-Eaton myasthenic syndrome patient

Neurology. 1994 Feb;44(2):334-8. doi: 10.1212/wnl.44.2.334.

Abstract

We investigated the heterogeneity of anti-voltage-gated calcium channel (VGCC) antibodies in the Lambert-Eaton myasthenic syndrome (LEMS) using a small-cell lung carcinoma line (MB) derived from an LEMS patient. Four of 13 LEMS patients had raised titers of anti-125I-omega-conotoxin-labeled (N-type) VGCCs, measured by radioimmunoassay using line MB as the source of antigen. Antagonists for L-type (nitrendipine and nifedipine) and N-type (omega-conotoxin) VGCCs inhibited K(+)-stimulated (voltage-dependent) Ca2+ flux into this line--by 22% for L-type and 2% for N-type at maximum concentration. Inhibition by the LEMS IgGs, by contrast, ranged from 46 to 78% at a concentration of 2 mg/ml. These differing effects on Ca2+ flux inhibition by LEMS IgGs on the one hand and by L- and N-type channel antagonists on the other, taken together with the observation that many of the sera failed to react with omega-conotoxin-labeled (N-type) channels in the immunoprecipitation assay, suggest that in many LEMS patients the autoantibodies target other VGCC subtypes besides L- or N-types, and that these are important in inducing the myasthenic disorder.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Autoantibodies / blood*
  • Autoantibodies / pharmacology*
  • Calcium / metabolism*
  • Calcium Channel Blockers / metabolism
  • Calcium Channel Blockers / pharmacology
  • Calcium Channels / drug effects
  • Calcium Channels / immunology*
  • Calcium Channels / metabolism
  • Carcinoma, Small Cell / metabolism*
  • Cell Line
  • Humans
  • Immunoglobulin G / blood
  • Immunoglobulin G / pharmacology
  • Kinetics
  • Lambert-Eaton Myasthenic Syndrome / blood
  • Lambert-Eaton Myasthenic Syndrome / immunology*
  • Lung Neoplasms / metabolism*
  • Middle Aged
  • Peptides / metabolism
  • Potassium / pharmacology
  • Tumor Cells, Cultured
  • omega-Conotoxins*

Substances

  • Autoantibodies
  • Calcium Channel Blockers
  • Calcium Channels
  • Immunoglobulin G
  • Peptides
  • omega-Conotoxins
  • Conus magus toxin
  • Potassium
  • Calcium