A 62-year-old man underwent successful coronary artery bypass for unstable angina 34 years after a complete repair of tetralogy of Fallot. Coronary risk factors were hypertension and a positive family history. While coronary disease was the presenting complaint, he had evidence of widespread atherosclerosis. He is the first patient reported to undergo coronary artery bypass following repair of tetralogy of Fallot. Coronary artery disease complicating tetralogy of Fallot has been mentioned five times in the literature. As the population of patients who have undergone tetralogy of Fallot ages, the number showing signs of coronary disease will likely rise. Thus, vigilance regarding risk factor modification must encompass these patients as they age.