[Waldman's disease. Primary intestinal lymphangiectasis]

Ann Dermatol Venereol. 1996;123(9):567-8.
[Article in French]

Abstract

Introduction: Primary intestinal lymphangiectasias are often associated with lymphoedema.

Observation: The diagnosis was performed at 4 months when Maxime presented with lymphoedema, diarrhea, hypoprotidemia and hypolipemia. Duodenum biopsies revealed intestinal lymphangiectasias. An hyperprotidic and low fat diet, medium chain triglyceride-supplemented and an elastic contention allowed a decline of the oedemas.

Discussion: We report one case of Waldman's disease. It shows very well the typical circumstances of diagnosis in this disease and the two types of oedema (lymphoedema and hypoprotidic oedema).

Publication types

  • English Abstract

MeSH terms

  • Dietary Proteins / administration & dosage
  • Humans
  • Infant
  • Lymphangiectasis, Intestinal / complications*
  • Lymphangiectasis, Intestinal / diet therapy
  • Lymphedema / complications*
  • Lymphedema / diet therapy
  • Male

Substances

  • Dietary Proteins