Severe ADAMTS13 deficiency in adult idiopathic thrombotic microangiopathies defines a subset of patients characterized by various autoimmune manifestations, lower platelet count, and mild renal involvement.
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Coppo P, et al. Among authors: bengoufa d.
Medicine (Baltimore). 2004 Jul;83(4):233-244. doi: 10.1097/01.md.0000133622.03370.07.
Medicine (Baltimore). 2004.
PMID: 15232311
Free article.