Bigger BW - Search Results

1

Macrophage enzyme and reduced inflammation drive brain correction of mucopolysaccharidosis IIIB by stem cell gene therapy.

Holley RJ, Ellison SM, Fil D, O'Leary C, McDermott J, Senthivel N, Langford-Smith AWW, Wilkinson FL, D'Souza Z, Parker H, Liao A, Rowlston S, Gleitz HFE, Kan SH, Dickson PI, Bigger BW. Holley RJ, et al. Among authors: bigger bw. Brain. 2018 Jan 1;141(1):99-116. doi: 10.1093/brain/awx311. Brain. 2018. PMID: 29186350

2

Genistein reduces lysosomal storage in peripheral tissues of mucopolysaccharide IIIB mice.

Malinowska M, Wilkinson FL, Bennett W, Langford-Smith KJ, O'Leary HA, Jakobkiewicz-Banecka J, Wynn R, Wraith JE, Wegrzyn G, Bigger BW. Malinowska M, et al. Among authors: bigger bw. Mol Genet Metab. 2009 Nov;98(3):235-42. doi: 10.1016/j.ymgme.2009.06.013. Epub 2009 Jun 27. Mol Genet Metab. 2009. PMID: 19632871

3

Evaluation of heparin cofactor II-thrombin complex as a biomarker on blood spots from mucopolysaccharidosis I, IIIA and IIIB mice.

Langford-Smith K, Arasaradnam M, Wraith JE, Wynn R, Bigger BW. Langford-Smith K, et al. Among authors: bigger bw. Mol Genet Metab. 2010 Mar;99(3):269-74. doi: 10.1016/j.ymgme.2009.10.175. Epub 2009 Oct 23. Mol Genet Metab. 2010. PMID: 19926322

4

Circadian rhythm and suprachiasmatic nucleus alterations in the mouse model of mucopolysaccharidosis IIIB.

Canal MM, Wilkinson FL, Cooper JD, Wraith JE, Wynn R, Bigger BW. Canal MM, et al. Among authors: bigger bw. Behav Brain Res. 2010 Jun 19;209(2):212-20. doi: 10.1016/j.bbr.2010.01.045. Epub 2010 Feb 4. Behav Brain Res. 2010. PMID: 20138090

5

Genistein improves neuropathology and corrects behaviour in a mouse model of neurodegenerative metabolic disease.

Malinowska M, Wilkinson FL, Langford-Smith KJ, Langford-Smith A, Brown JR, Crawford BE, Vanier MT, Grynkiewicz G, Wynn RF, Wraith JE, Wegrzyn G, Bigger BW. Malinowska M, et al. Among authors: bigger bw. PLoS One. 2010 Dec 1;5(12):e14192. doi: 10.1371/journal.pone.0014192. PLoS One. 2010. PMID: 21152017 Free PMC article.

6

Hyperactive behaviour in the mouse model of mucopolysaccharidosis IIIB in the open field and home cage environments.

Langford-Smith A, Malinowska M, Langford-Smith KJ, Wegrzyn G, Jones S, Wynn R, Wraith JE, Wilkinson FL, Bigger BW. Langford-Smith A, et al. Among authors: bigger bw. Genes Brain Behav. 2011 Aug;10(6):673-82. doi: 10.1111/j.1601-183X.2011.00706.x. Epub 2011 Jun 29. Genes Brain Behav. 2011. PMID: 21635693 Free article.

7

Trial and error: how the unclonable human mitochondrial genome was cloned in yeast.

Bigger BW, Liao AY, Sergijenko A, Coutelle C. Bigger BW, et al. Pharm Res. 2011 Nov;28(11):2863-70. doi: 10.1007/s11095-011-0527-1. Epub 2011 Jul 9. Pharm Res. 2011. PMID: 21739320

8

Mucopolysaccharidosis type I, unique structure of accumulated heparan sulfate and increased N-sulfotransferase activity in mice lacking α-l-iduronidase.

Holley RJ, Deligny A, Wei W, Watson HA, Niñonuevo MR, Dagälv A, Leary JA, Bigger BW, Kjellén L, Merry CL. Holley RJ, et al. Among authors: bigger bw. J Biol Chem. 2011 Oct 28;286(43):37515-24. doi: 10.1074/jbc.M111.287474. Epub 2011 Aug 26. J Biol Chem. 2011. PMID: 21873421 Free PMC article.

9

Female mucopolysaccharidosis IIIA mice exhibit hyperactivity and a reduced sense of danger in the open field test.

Langford-Smith A, Langford-Smith KJ, Jones SA, Wynn RF, Wraith JE, Wilkinson FL, Bigger BW. Langford-Smith A, et al. Among authors: bigger bw. PLoS One. 2011;6(10):e25717. doi: 10.1371/journal.pone.0025717. Epub 2011 Oct 18. PLoS One. 2011. PMID: 22028789 Free PMC article.

10

Hematopoietic stem cell and gene therapy corrects primary neuropathology and behavior in mucopolysaccharidosis IIIA mice.

Langford-Smith A, Wilkinson FL, Langford-Smith KJ, Holley RJ, Sergijenko A, Howe SJ, Bennett WR, Jones SA, Wraith J, Merry CL, Wynn RF, Bigger BW. Langford-Smith A, et al. Among authors: bigger bw. Mol Ther. 2012 Aug;20(8):1610-21. doi: 10.1038/mt.2012.82. Epub 2012 May 1. Mol Ther. 2012. PMID: 22547151 Free PMC article.

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