The Impact of Mitochondrial Dysfunction on Dopaminergic Neurons in the Olfactory Bulb and Odor Detection

Mol Neurobiol. 2020 Sep;57(9):3646-3657. doi: 10.1007/s12035-020-01947-w. Epub 2020 Jun 20.

Abstract

Understanding non-motor symptoms of Parkinson's disease is important in order to unravel the underlying molecular mechanisms of the disease. Olfactory dysfunction is an early stage, non-motor symptom which occurs in 95% of Parkinson's disease patients. Mitochondrial dysfunction is a key feature in Parkinson's disease and importantly contributes to the selective loss of dopaminergic neurons the substantia nigra pars compacta. The olfactory bulb, the first olfactory processing station, also contains dopaminergic neurons, which modulate odor information and thereby enable odor detection as well as odor discrimination. MitoPark mice are a genetic model for Parkinson's disease with severe mitochondrial dysfunction, reproducing the differential vulnerability of dopaminergic neurons in the midbrain. These animals were used to investigate the impact of mitochondrial dysfunction on olfactory-related behavior and olfactory bulb dopaminergic neuron survival. Odor detection was severely impaired in MitoPark mice. Interestingly, only the small anaxonic dopaminergic subpopulation, which is continuously replenished by neurogenesis, was moderately reduced in number, much less compared with dopaminergic neurons in the midbrain. As a potential compensatory response, an enhanced mobilization of progenitor cells was found in the subventricular zone. These results reveal a high robustness of dopaminergic neurons located in the olfactory bulb towards mitochondrial impairment, in striking contrast to their midbrain counterparts.

Keywords: Mitochondrial dysfunction; Neurogenesis; Olfactory bulb; Parkinson’s disease.

MeSH terms

  • Animals
  • Cell Count
  • DNA-Binding Proteins / metabolism
  • Dopaminergic Neurons / pathology*
  • Electron Transport
  • High Mobility Group Proteins / metabolism
  • Mesencephalon / pathology
  • Mice, Inbred C57BL
  • Mitochondria / pathology*
  • Neostriatum / metabolism
  • Nerve Degeneration / pathology
  • Odorants*
  • Olfactory Bulb / pathology*
  • PAX6 Transcription Factor / metabolism
  • Stem Cells / metabolism
  • Substantia Nigra / metabolism
  • Time Factors
  • Tyrosine 3-Monooxygenase / metabolism

Substances

  • DNA-Binding Proteins
  • High Mobility Group Proteins
  • PAX6 Transcription Factor
  • Tfam protein, mouse
  • Tyrosine 3-Monooxygenase